Reaction: B4GALT7 transfers Gal group to xylosyl-unit of the tetrasaccharide linker
Beta-1,4-galactosyltransferase 7 (B4GALT7) adds galactose (Gal) to beta-xyloside in a beta-1,4 linkage creating the second unit in the formation of the tetrasaccharide linker, the precursor required for glycosaminoglycan (GAG) synthesis (Almeida et al. 1999). Defects in B4GALT7 cause Ehlers-Danlos syndrome progeroid type (EDSP) (MIM:130070) (Okajima et al. 1999).
Reaction - small molecule participants:
UDP [Golgi lumen]
UDP-Gal [Golgi lumen]
Reactome.org reaction link: R-HSA-1889981
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Reaction input - small molecules:
UDP-alpha-D-galactose(2-)
Reaction output - small molecules:
UDP(3-)
Reactome.org link: R-HSA-1889981